Síndrome PFAPA: Diagnóstico e Tratamento na Atenção Primária à Saúde

Laniel Aparecido Bueno, Débora Magalhães Paiva, Paulo Henrique Pimenta de Carvalho

Resumo


Objetivo: Apresentar informações sobre o diagnóstico e tratamento da síndrome PFAPA na Atenção Primária à Saúde. Métodos: Revisão sistemática de literatura baseada na recomendação PRISMA e realizada nas bases de dados Scielo, Lilacs, Medline, IBECS e PubMed, incluindo estudos publicados no período de 2004 a 2018, além da consulta a outros documentos específicos da síndrome PFAPA. Resultados: Após busca e seleção, foram incluídos 31 artigos. Avaliação e Diagnóstico: A síndrome PFAPA acomete principalmente crianças, sendo caracterizada por febre periódica acompanhada por faringite, estomatite aftosa e/ou adenite cervical. Seu diagnóstico é clínico e por exclusão, baseado em critérios estabelecidos. Recomendações: Os episódios costumam responder a prednisona e, em graus variáveis, a cimetidina e colchicina. Casos refratários e acompanhados de hipertrofia tonsilar são candidatos a tonsilectomia, devendo ser encaminhados à avaliação otorrinolaringológica.


Palavras-chave


Febre Recorrente; Faringite; Estomatite Aftosa; Adenite; Atenção Primária à Saúde

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Referências


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DOI: https://doi.org/10.5712/rbmfc14(41)1815

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Direitos autorais 2019 Laniel Aparecido Bueno, Débora Magalhães Paiva, Paulo Henrique Pimenta de Carvalho

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